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Official Description

Repair of hypoplastic or interrupted aortic arch using autogenous or prosthetic material; without cardiopulmonary bypass

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

The procedure described by CPT® Code 33852 involves the surgical repair of a hypoplastic or interrupted aortic arch, which is a critical condition affecting the aorta. A hypoplastic aortic arch, also known as diffuse long-segment coarctation, is characterized by a narrowing of the aorta along its entire arch, leading to potential complications in blood flow. An interrupted aortic arch, on the other hand, refers to a complete absence of a segment of the aortic arch, which can severely impact the circulatory system. These conditions often coexist with other congenital cardiac anomalies, such as ventricular septal defect (VSD), patent ductus arteriosus (PDA), aortopulmonary window, and truncus arteriosus, necessitating careful surgical intervention. The surgical approach typically involves making a posterolateral incision to gain access to the aortic arch, followed by mobilization of the ascending aorta, aortic arch, its branches, ductus arteriosus, and descending aorta. During the procedure, it is crucial to protect the recurrent laryngeal and phrenic nerves, and lymphatic vessels are managed with hemoclips. The ductus arteriosus is ligated to prevent blood flow through this vessel. The repair can be performed without cardiopulmonary bypass, utilizing a partial occluding clamp across the aortic arch, or with cardiopulmonary bypass, where cannulation of the aorta and vena cavae is performed to establish bypass and cross-clamp the aorta. The actual repair of the hypoplastic or interrupted segment can be achieved through various techniques, including patch aortoplasty, tube graft replacement, or the use of an autogenous graft, such as a left subclavian artery flap graft. After the repair, the parietal pleura is closed over the graft, and the chest incisions are sutured, with chest tubes placed as necessary to facilitate recovery.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure is indicated for patients with the following conditions:

  • Hypoplastic Aortic Arch - A condition characterized by a narrowing of the aorta along the entire arch, which can lead to significant cardiovascular complications.
  • Interrupted Aortic Arch - A congenital defect where a segment of the aortic arch is completely absent, necessitating surgical intervention to restore normal blood flow.
  • Associated Cardiac Anomalies - Conditions such as ventricular septal defect (VSD), patent ductus arteriosus (PDA), aortopulmonary window, and truncus arteriosus that may coexist with hypoplastic or interrupted aortic arch, requiring comprehensive surgical management.

2. Procedure

The surgical procedure for repairing a hypoplastic or interrupted aortic arch involves several critical steps:

  • Accessing the Aortic Arch - A posterolateral incision is made to provide access to the aortic arch. The parietal pleura is incised to facilitate exposure of the underlying structures.
  • Mobilization of Aortic Structures - The ascending aorta, aortic arch, its branches, ductus arteriosus, and descending aorta are carefully mobilized to allow for adequate surgical intervention. This step is crucial for ensuring that all necessary components are accessible for repair.
  • Protection of Nerves and Vessels - During the procedure, care is taken to protect the recurrent laryngeal and phrenic nerves to prevent postoperative complications. Lymphatic vessels are controlled using hemoclips to minimize bleeding.
  • Ligation of Ductus Arteriosus - The ductus arteriosus is ligated to eliminate abnormal blood flow through this vessel, which is essential for proper circulation post-repair.
  • Application of Occluding Clamp - If the procedure is performed without cardiopulmonary bypass, a partial occluding clamp is applied across the aortic arch to facilitate the repair. If cardiopulmonary bypass is utilized, the aorta and superior and inferior vena cava are cannulated, and bypass is established with the aorta cross-clamped.
  • Repair of the Aortic Arch - The hypoplastic or interrupted segment of the aortic arch is repaired using one of several techniques. Patch aortoplasty involves making a longitudinal incision beyond the narrowed section, followed by the placement of a synthetic patch that is sutured in place. Alternatively, a tube graft may be used to replace the missing segment of the aortic arch. Another option is the placement of an autogenous graft, such as a left subclavian artery flap graft, to restore continuity.
  • Closure of Incisions - After the repair is completed, the parietal pleura is closed over the graft, and the chest incisions are sutured. Chest tubes may be placed as needed to facilitate drainage and support recovery.

3. Post-Procedure

Post-procedure care involves monitoring the patient for any complications related to the surgery. Expected recovery includes observation for proper healing of the surgical site and management of any potential issues such as bleeding or infection. The placement of chest tubes, if utilized, will aid in the removal of any excess fluid or air from the pleural space, promoting optimal recovery. Follow-up evaluations will be necessary to assess the success of the repair and the overall cardiovascular function of the patient.

Short Descr RPR HYPOPL A-ARCH WO BYP
Medium Descr RPR HYPOPLASTIC A-ARCH W/AUTOG/PROSTC W/O BYPASS
Long Descr Repair of hypoplastic or interrupted aortic arch using autogenous or prosthetic material; without cardiopulmonary bypass
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 0 - Co-surgeons not permitted for this procedure.
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 52 - Aortic resection, replacement or anastomosis

This is a primary code that can be used with these additional add-on codes.

33257 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure)
33258 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), without cardiopulmonary bypass (List separately in addition to code for primary procedure)
Date
Action
Notes
2025-01-01 Changed Short and Medium Descriptions changed.
1990-01-01 Added First appearance in code book in 1990.
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