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Official Description

Repair, congenital arteriovenous fistula; extremities

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

A congenital arteriovenous fistula is a vascular anomaly characterized by an abnormal connection between an artery and a vein that is present from birth. This condition can manifest in various locations throughout the vascular system and can differ significantly in terms of size and length. The presence of this abnormal communication allows blood to flow from the artery into the vein under high pressure. Since the walls of veins are not designed to withstand such high-pressure blood flow, they can become distended, leading to an enlargement of the venous structure. This increased blood flow can result in various cardiovascular complications over time. Repairing congenital arteriovenous fistulas can be particularly challenging due to their potential extension into surrounding anatomical structures. To facilitate the repair process, angiography may be performed to accurately map the course of the fistula. The surgical procedure involves exposing the fistula, isolating it from surrounding tissues, and then severing the abnormal connection. The artery and vein are subsequently repaired, either with sutures or by using a synthetic patch or vein graft, ensuring that normal blood flow is restored. This procedure is specifically designated for cases involving the extremities, distinguishing it from similar repairs in other anatomical regions.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure for repairing a congenital arteriovenous fistula in the extremities is indicated for patients presenting with the following conditions:

  • Congenital arteriovenous fistula - An abnormal communication between an artery and vein that is present at birth, which may lead to complications if left untreated.
  • Enlargement of venous structures - Due to high-pressure blood flow from the artery, the venous walls may stretch and enlarge, necessitating repair to prevent further cardiovascular issues.
  • Cardiovascular complications - Potential complications arising from the abnormal blood flow, which may include heart failure or other related conditions.

2. Procedure

The procedure for repairing a congenital arteriovenous fistula in the extremities involves several critical steps:

  • Angiography - Initially, a separate angiography is performed to delineate the course of the arteriovenous fistula. This imaging technique helps the physician visualize the anatomy and plan the surgical approach effectively.
  • Exposure of the fistula - The surgeon then makes an incision to expose the fistula. This step involves careful dissection to free the fistula from surrounding tissues, ensuring that the surgical field is clear for the repair.
  • Clamping - Once the fistula is adequately exposed, clamps are placed on both the artery and the vein. This isolation is crucial as it prevents blood flow during the repair process, allowing for a safer and more controlled environment.
  • Severing the fistulous communication - The abnormal connection between the artery and vein is then severed. This step is essential to eliminate the high-pressure flow from the artery into the vein.
  • Repair of the artery and vein - After severing the fistula, the artery and vein are repaired. This can be accomplished using sutures to close the vessels or, in some cases, a synthetic patch or vein graft may be employed to ensure proper healing and restoration of normal blood flow.
  • Checking hemostasis - Once the repairs are completed, the clamps are removed, and the surgeon checks for hemostasis to ensure that there is no excessive bleeding at the repair site.
  • Closure of overlying tissues - Finally, the overlying tissues are closed in layers to promote optimal healing and restore the integrity of the skin and surrounding structures.

3. Post-Procedure

Post-procedure care for patients who have undergone repair of a congenital arteriovenous fistula in the extremities typically includes monitoring for any signs of complications, such as bleeding or infection at the surgical site. Patients may be advised to limit physical activity for a specified period to allow for proper healing. Follow-up appointments are essential to assess the success of the repair and to ensure that normal blood flow has been restored without any recurrence of the fistula. Additionally, patients may require imaging studies in the future to monitor the vascular status of the affected area.

Short Descr RPR CGEN AV FISTULA XTR
Medium Descr REPAIR CONGENITAL AV FISTULA EXTREMITIES
Long Descr Repair, congenital arteriovenous fistula; extremities
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Hospital Part B services paid through a comprehensive APC
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 2
CCS Clinical Classification 61 - Other OR procedures on vessels other than head and neck
51 Multiple procedures: when multiple procedures, other than e/m services, physical medicine and rehabilitation services or provision of supplies (eg, vaccines), are performed at the same session by the same individual, the primary procedure or service may be reported as listed. the additional procedure(s) or service(s) may be identified by appending modifier 51 to the additional procedure or service code(s). note: this modifier should not be appended to designated "add-on" codes (see appendix d).
59 Distinct procedural service: under certain circumstances, it may be necessary to indicate that a procedure or service was distinct or independent from other non-e/m services performed on the same day. modifier 59 is used to identify procedures/services, other than e/m services, that are not normally reported together, but are appropriate under the circumstances. documentation must support a different session, different procedure or surgery, different site or organ system, separate incision/excision, separate lesion, or separate injury (or area of injury in extensive injuries) not ordinarily encountered or performed on the same day by the same individual. however, when another already established modifier is appropriate it should be used rather than modifier 59. only if no more descriptive modifier is available, and the use of modifier 59 best explains the circumstances, should modifier 59 be used. note: modifier 59 should not be appended to an e/m service. to report a separate and distinct e/m service with a non-e/m service performed on the same date, see modifier 25.
78 Unplanned return to the operating/procedure room by the same physician or other qualified health care professional following initial procedure for a related procedure during the postoperative period: it may be necessary to indicate that another procedure was performed during the postoperative period of the initial procedure (unplanned procedure following initial procedure). when this procedure is related to the first, and requires the use of an operating/procedure room, it may be reported by adding modifier 78 to the related procedure. (for repeat procedures, see modifier 76.)
79 Unrelated procedure or service by the same physician or other qualified health care professional during the postoperative period: the individual may need to indicate that the performance of a procedure or service during the postoperative period was unrelated to the original procedure. this circumstance may be reported by using modifier 79. (for repeat procedures on the same day, see modifier 76.)
80 Assistant surgeon: surgical assistant services may be identified by adding modifier 80 to the usual procedure number(s).
82 Assistant surgeon (when qualified resident surgeon not available): the unavailability of a qualified resident surgeon is a prerequisite for use of modifier 82 appended to the usual procedure code number(s).
AS Physician assistant, nurse practitioner, or clinical nurse specialist services for assistant at surgery
GC This service has been performed in part by a resident under the direction of a teaching physician
LT Left side (used to identify procedures performed on the left side of the body)
RT Right side (used to identify procedures performed on the right side of the body)
Date
Action
Notes
2025-01-01 Changed Short and Medium Descriptions changed.
2013-01-01 Changed Medium Descriptor changed.
Pre-1990 Added Code added.
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