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Official Description

Repair of omphalocele (Gross type operation); second stage

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

An omphalocele is a congenital defect characterized by a failure of the abdominal wall to close properly, resulting in the protrusion of intra-abdominal organs through the abdominal wall at the umbilical ring. This defect is marked by the absence of abdominal muscles, fascia, and skin, with the protruding structures being covered by a membrane composed of peritoneum and amnion. The classic presentation of an omphalocele involves the umbilical cord being attached to the sac that contains the herniated organs. The surgical repair of an omphalocele is typically performed in two stages. The first stage involves the ligation of umbilical vessels, amputation of the umbilical cord, and the creation of skin flaps to cover the defect, which results in a large ventral hernia. The second stage, which is denoted by CPT® Code 49611, is performed at a later date, usually between six months to two years after the initial repair. During this stage, the previously created skin flaps are reopened, and the ventral hernia is repaired, restoring the integrity of the abdominal wall.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The repair of an omphalocele is indicated for patients presenting with this congenital defect, which may be diagnosed at birth or during prenatal imaging. The procedure is necessary to address the protrusion of intra-abdominal organs and to prevent complications such as infection, strangulation of the herniated organs, and other associated morbidity. The timing of the second stage repair is typically determined based on the patient's growth and development, as well as the condition of the skin flaps and the hernia.

  • Congenital Omphalocele The primary indication for the procedure is the presence of an omphalocele, which requires surgical intervention to repair the abdominal wall defect.
  • Prevention of Complications The procedure aims to prevent potential complications associated with the herniated organs, including infection and strangulation.
  • Restoration of Abdominal Wall Integrity The repair is necessary to restore the normal anatomy and function of the abdominal wall.

2. Procedure

The procedure for the second stage repair of an omphalocele, coded as CPT® 49611, involves several critical steps to ensure the successful closure of the abdominal wall defect. The first step is to carefully reopen the previously created skin flaps that were developed during the first stage of the repair. This is done with precision to avoid damaging the underlying tissues. Once the skin flaps are opened, the surgeon assesses the condition of the herniated organs and the surrounding tissues. The next step involves the careful reduction of the herniated contents back into the abdominal cavity. This step is crucial as it allows for the restoration of normal anatomical positioning of the intra-abdominal structures. After the reduction, the surgeon proceeds to repair the abdominal wall defect. This is typically achieved by suturing the fascia and muscle layers together, ensuring that the abdominal wall is reinforced and secure. Finally, the skin flaps are closed over the repaired area, completing the procedure and restoring the integrity of the abdominal wall.

  • Step 1: Reopening Skin Flaps The surgeon carefully reopens the skin flaps that were created during the first stage of the repair to access the herniated organs.
  • Step 2: Assessment of Herniated Organs The condition of the herniated organs and surrounding tissues is assessed to ensure they are viable and can be safely reduced.
  • Step 3: Reduction of Herniated Contents The herniated organs are gently reduced back into the abdominal cavity, restoring their normal anatomical position.
  • Step 4: Repair of Abdominal Wall Defect The abdominal wall defect is repaired by suturing the fascia and muscle layers together, reinforcing the abdominal wall.
  • Step 5: Closure of Skin Flaps The skin flaps are then closed over the repaired area, completing the surgical procedure.

3. Post-Procedure

After the second stage repair of an omphalocele, patients typically require close monitoring for any signs of complications, such as infection or issues with the healing of the surgical site. Post-operative care may include pain management, wound care, and monitoring for any signs of hernia recurrence. The expected recovery period can vary, but patients are generally advised to avoid strenuous activities for a specified duration to allow for proper healing. Follow-up appointments are essential to assess the surgical site and ensure that the abdominal wall is healing appropriately. Additional interventions may be necessary if complications arise during the recovery process.

Short Descr REPAIR UMBILICAL LESION
Medium Descr RPR OMPHALOCELE GROSS TYP OPRATION 2ND STG
Long Descr Repair of omphalocele (Gross type operation); second stage
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P1G - Major procedure - Other
MUE 1
CCS Clinical Classification 86 - Other hernia repair

This is a primary code that can be used with these additional add-on codes.

49623 Add-on Code Resequenced Code MPFS Status: Active Code APC N Removal of total or near total non-infected mesh or other prosthesis at the time of initial or recurrent anterior abdominal hernia repair or parastomal hernia repair, any approach (ie, open, laparoscopic, robotic) (List separately in addition to code for primary procedure)
Date
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Notes
2011-01-01 Changed Guideline information changed.
Pre-1990 Added Code added.
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