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Official Description

Repair of double outlet right ventricle with intraventricular tunnel repair; with repair of right ventricular outflow tract obstruction

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

The procedure described by CPT® Code 33612 involves the surgical repair of a double outlet right ventricle (DORV) with the use of an intraventricular tunnel repair, in conjunction with the correction of right ventricular outflow tract obstruction. DORV is a congenital heart defect characterized by both the aorta and pulmonary artery originating from the right ventricle, which can lead to significant hemodynamic complications. In this procedure, the surgeon creates an intraventricular tunnel, which serves as a conduit for blood flow from the left ventricle through a ventricular septal defect (VSD) to the aorta. This is crucial for ensuring adequate oxygenation of the blood, as the left ventricle typically supplies oxygen-rich blood to the body. The surgical approach begins with the establishment of cardiopulmonary bypass, allowing the heart to be temporarily stopped and providing a bloodless field for the operation. The right atrium is incised to gain access to the heart's internal structures, where the VSD is visualized and assessed in relation to the aorta. Depending on the size and position of the VSD, the surgeon may either approach it through the tricuspid valve or make an incision in the right ventricle. The creation of the tunnel involves careful dissection and suturing techniques to ensure that the new pathway for blood flow is both functional and anatomically correct. In addition to the tunnel repair, the procedure addresses any obstruction in the right ventricular outflow tract, which may occur due to the bulging of the tunnel. This is rectified by enlarging the right ventricle with an autologous pericardial patch, which is a piece of the patient's own pericardium used to reinforce the heart structure. The meticulous nature of this surgery requires a thorough understanding of cardiac anatomy and surgical techniques to achieve optimal outcomes for patients with this complex congenital condition.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure described by CPT® Code 33612 is indicated for patients diagnosed with double outlet right ventricle (DORV), a congenital heart defect where both the aorta and pulmonary artery arise from the right ventricle. This condition often coexists with a ventricular septal defect (VSD), which is critical for blood flow from the left ventricle. The indications for performing this surgical repair include:

  • Double Outlet Right Ventricle (DORV) - A congenital heart defect requiring surgical intervention to correct abnormal blood flow.
  • Ventricular Septal Defect (VSD) - The presence of a VSD that necessitates repair to facilitate proper blood circulation from the left ventricle to the aorta.
  • Right Ventricular Outflow Tract Obstruction - Obstruction that may occur due to the anatomical configuration of the heart, which can lead to compromised cardiac function.

2. Procedure

The surgical procedure for CPT® Code 33612 involves several critical steps to repair the DORV and address the right ventricular outflow tract obstruction:

  • Establishment of Cardiopulmonary Bypass - The procedure begins with the establishment of cardiopulmonary bypass through bicaval cannulation, allowing the heart to be temporarily stopped and providing a bloodless surgical field.
  • Incision of the Right Atrium - The surgeon makes an incision in the right atrium to access the heart's internal structures and inspect the anatomy.
  • Visualization of the VSD - The ventricular septal defect is visualized through the tricuspid valve, and its relationship to the aorta is assessed to determine the best approach for repair.
  • Approach to the VSD - Depending on the size and position of the VSD, the surgeon may approach it through the tricuspid valve or by incising the right ventricle.
  • Enlargement of the VSD - If the circumference of the VSD is smaller than the tunnel, the surgeon enlarges the VSD by incising the ventricular septum superiorly and anteriorly, taking care to avoid damaging the conduction tissue.
  • Creation of the Intraventricular Tunnel - A tunnel is created using pericardium, polytetrafluoroethylene (PTFE), or other synthetic materials, matching the circumference of the aorta and running from the anterior portion of the aorta to the VSD.
  • Suturing the Tunnel - Sutures are placed through the base of the tricuspid valve leaflet and the midportion of the tunnel, with additional sutures securing the tunnel to the inferior and posterior rim of the VSD.
  • Closure of the VSD - If the VSD is larger than the tunnel, the remaining opening is closed after securing the tunnel in place.
  • Correction of Right Ventricular Outflow Tract Obstruction - The surgeon then addresses the right ventricular outflow tract obstruction by enlarging the right ventricle using an autologous pericardial patch.
  • Closure of Incisions - Finally, the incisions in the right atrium and right ventricle are closed, completing the surgical repair.

3. Post-Procedure

Post-procedure care following the repair of DORV with CPT® Code 33612 involves close monitoring of the patient in a postoperative setting. Patients typically require intensive care to manage hemodynamic stability and monitor for any complications. Recovery may include pain management, monitoring for signs of infection, and ensuring proper cardiac function. Follow-up echocardiograms may be necessary to assess the success of the repair and the function of the heart structures. The length of recovery can vary based on the individual patient's condition and response to surgery.

Short Descr REPAIR DOUBLE VENTRICLE
Medium Descr RPR 2 OUTLET R VNTRC RPR R VENTR O/F TRC OBSTRCJ
Long Descr Repair of double outlet right ventricle with intraventricular tunnel repair; with repair of right ventricular outflow tract obstruction
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 49 - Other OR heart procedures

This is a primary code that can be used with these additional add-on codes.

33257 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure)
33259 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure)
33924 Addon Code MPFS Status: Active Code APC C CPT Assistant Article Ligation and takedown of a systemic-to-pulmonary artery shunt, performed in conjunction with a congenital heart procedure (List separately in addition to code for primary procedure)
34714 Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure)
34716 Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure)
34833 Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure)
51 Multiple procedures: when multiple procedures, other than e/m services, physical medicine and rehabilitation services or provision of supplies (eg, vaccines), are performed at the same session by the same individual, the primary procedure or service may be reported as listed. the additional procedure(s) or service(s) may be identified by appending modifier 51 to the additional procedure or service code(s). note: this modifier should not be appended to designated "add-on" codes (see appendix d).
80 Assistant surgeon: surgical assistant services may be identified by adding modifier 80 to the usual procedure number(s).
RT Right side (used to identify procedures performed on the right side of the body)
Date
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1994-01-01 Added First appearance in code book in 1994.
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