Coding Ahead
CasePilot
Medical Coding Assistant
Case2Code
Search and Code Lookup Tool
RedactPHI
HIPAA-Compliant PHI Redaction
DetectICD10CM
ICD-10-CM Code Detection
Log in Register free account
1 code page views remaining. Guest accounts are limited to 1 page view. Register free account to get 5 more views.
Log in Register free account

Official Description

Direct or patch closure, sinus venosus, with or without anomalous pulmonary venous drainage

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

Direct or patch closure of a sinus venosus type defect is a surgical procedure aimed at correcting a specific type of atrial septal defect known as sinus venosus atrial septal defect (SVASD). This defect is characterized by an abnormal opening in the upper part of the atrial septum, which separates the right and left atria of the heart. The most prevalent form of this defect is located near the superior vena cava, often accompanied by anomalous pulmonary venous drainage, where the right upper pulmonary vein drains into the superior vena cava instead of the left atrium. There are variations of this defect, including one that occurs at the junction of the right atrium and inferior vena cava, which may involve the right lower pulmonary vein draining into the inferior vena cava. The least common variant is situated posterior to the fossa ovalis and does not involve the major venous structures. The surgical approach typically involves a median sternotomy or an upper hemisternotomy to access the heart. Once the heart is accessed, cardiopulmonary bypass is established to maintain circulation while the heart is temporarily stopped. The procedure involves incising the right atrium to expose the defect, followed by either direct suturing for smaller defects or the use of a patch graft for larger defects that involve the vena cava. This intervention not only closes the septal defect but also corrects any associated anomalous pulmonary venous drainage, thereby restoring normal blood flow within the heart.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure of direct or patch closure of a sinus venosus type defect is indicated for the following conditions:

  • Sinus Venosus Atrial Septal Defect (SVASD) This defect is characterized by an abnormal opening in the atrial septum, typically located near the superior vena cava, which can lead to significant hemodynamic changes and complications if left untreated.
  • Anomalous Pulmonary Venous Drainage This condition occurs when one or more pulmonary veins drain into the wrong chamber of the heart, often associated with SVASD, necessitating surgical intervention to restore normal anatomy and function.
  • Right Atrial Volume Overload Patients may present with symptoms related to increased volume in the right atrium due to the left-to-right shunt caused by the defect, which can lead to heart failure or arrhythmias.

2. Procedure

The procedure for direct or patch closure of a sinus venosus type defect involves several critical steps:

  • Step 1: Surgical Access The heart is accessed through a median sternotomy or an upper hemisternotomy, allowing the surgeon to reach the cardiac structures effectively.
  • Step 2: Establishing Cardiopulmonary Bypass Venous and arterial cannulas are inserted to establish cardiopulmonary bypass, which temporarily takes over the function of the heart and lungs, allowing for a bloodless surgical field.
  • Step 3: Inducing Cardioplegic Arrest Cardioplegic arrest is initiated to stop the heart, providing a still and safe environment for the surgical repair of the defect.
  • Step 4: Atriotomy The right atrium is incised (atriotomy) to expose the sinus venosus defect, allowing the surgeon to visualize and assess the size and nature of the defect.
  • Step 5: Repairing the Defect If the defect is small and does not involve the superior or inferior vena cava, it is repaired using sutures. For larger defects that involve the vena cava, closure is achieved using a pericardial tissue or synthetic patch graft.
  • Step 6: Configuring the Patch The patch is placed over the defect and configured to redirect blood flow from the pulmonary vein into the left atrium, effectively closing the septal defect and correcting the anomalous pulmonary venous drainage.
  • Step 7: Ligation of the Azygos Vein The azygos vein may be ligated to prevent it from draining into the left atrium, which is an important step in ensuring proper blood flow post-repair.
  • Step 8: Closing the Atrial Incision Following the successful repair of the sinus venosus defect, the right atrial incision is closed securely.
  • Step 9: Weaning Off Bypass The patient is then weaned off cardiopulmonary bypass, allowing the heart to resume its normal function.
  • Step 10: Postoperative Care Chest tubes are placed as needed to manage any fluid accumulation, and the chest incision is closed to complete the procedure.

3. Post-Procedure

After the procedure, patients typically require close monitoring in a postoperative setting. Expected recovery includes observation for any complications such as bleeding or infection. The placement of chest tubes may be necessary to drain any excess fluid or air from the thoracic cavity. Patients are usually weaned off ventilatory support as they stabilize. The overall recovery time can vary based on individual patient factors, but many patients can expect to resume normal activities within a few weeks, pending their physician's guidance. Follow-up appointments are essential to monitor heart function and ensure the success of the repair.

Short Descr REVISION OF HEART VEINS
Medium Descr DIR/PTCH CLS SINUS VENOSUS W/WO ANOM PUL VEN DRG
Long Descr Direct or patch closure, sinus venosus, with or without anomalous pulmonary venous drainage
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 49 - Other OR heart procedures

This is a primary code that can be used with these additional add-on codes.

33257 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure)
33259 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure)
34714 Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure)
34716 Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure)
34833 Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure)
51 Multiple procedures: when multiple procedures, other than e/m services, physical medicine and rehabilitation services or provision of supplies (eg, vaccines), are performed at the same session by the same individual, the primary procedure or service may be reported as listed. the additional procedure(s) or service(s) may be identified by appending modifier 51 to the additional procedure or service code(s). note: this modifier should not be appended to designated "add-on" codes (see appendix d).
62 Two surgeons: when 2 surgeons work together as primary surgeons performing distinct part(s) of a procedure, each surgeon should report his/her distinct operative work by adding modifier 62 to the procedure code and any associated add-on code(s) for that procedure as long as both surgeons continue to work together as primary surgeons. each surgeon should report the co-surgery once using the same procedure code. if additional procedure(s) (including add-on procedure(s) are performed during the same surgical session, separate code(s) may also be reported with modifier 62 added. note: if a co-surgeon acts as an assistant in the performance of additional procedure(s), other than those reported with the modifier 62, during the same surgical session, those services may be reported using separate procedure code(s) with modifier 80 or modifier 82 added, as appropriate.
80 Assistant surgeon: surgical assistant services may be identified by adding modifier 80 to the usual procedure number(s).
82 Assistant surgeon (when qualified resident surgeon not available): the unavailability of a qualified resident surgeon is a prerequisite for use of modifier 82 appended to the usual procedure code number(s).
AS Physician assistant, nurse practitioner, or clinical nurse specialist services for assistant at surgery
GC This service has been performed in part by a resident under the direction of a teaching physician
RT Right side (used to identify procedures performed on the right side of the body)
Date
Action
Notes
Pre-1990 Added Code added.
Code
Description
Code
Description
Code
Description
Code
Description
Code
Description
CasePilot

Get instant expert-level medical coding assistance.

Ask about:
CPT Codes Guidelines Modifiers Crosswalks NCCI Edits Compliance Medicare Coverage
Example: "What is CPT code 99213?" or "Guidelines for E/M services"