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Official Description

Complete repair tetralogy of Fallot without pulmonary atresia;

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

The procedure described by CPT® Code 33692 involves the complete surgical repair of tetralogy of Fallot (TOF) in neonates, specifically when pulmonary atresia is not present. Tetralogy of Fallot is a complex congenital heart defect characterized by four specific abnormalities: pulmonary stenosis, right ventricular hypertrophy, ventricular septal defect (VSD), and overriding aorta. Pulmonary stenosis refers to the narrowing of the pulmonary valve and the outflow tract, which obstructs blood flow from the right ventricle to the pulmonary artery. This obstruction leads to increased pressure in the right ventricle, resulting in right ventricular hypertrophy, which is the thickening of the muscular walls of the right ventricle. The VSD is a defect that consists of one or more holes in the ventricular septum, allowing for abnormal blood flow between the heart's ventricles. The overriding aorta is a condition where the aorta is positioned directly above the VSD, receiving blood from both the right and left ventricles, which can lead to mixing of oxygenated and deoxygenated blood. During the surgical procedure, the heart is accessed through a median sternotomy, and cardiopulmonary bypass is established to maintain circulation while the heart is stopped using cardioplegic arrest. The VSD is repaired using a synthetic patch, which effectively closes the defect and prevents the mixing of blood. The pulmonary valve is addressed by resecting obstructive tissue to alleviate the stenosis, and if necessary, a transannular patch may be placed to enlarge the outflow tract. In cases where pulmonary atresia is present, a conduit is created from the right ventricle to the pulmonary artery to ensure proper blood flow to the lungs. This comprehensive approach aims to correct the anatomical defects associated with TOF, allowing for improved oxygenation and overall cardiac function in the neonate.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure is indicated for neonates diagnosed with tetralogy of Fallot (TOF) without pulmonary atresia. The following conditions are typically present:

  • Pulmonary Stenosis - A narrowing of the pulmonary valve and outflow tract that obstructs blood flow from the right ventricle.
  • Right Ventricular Hypertrophy - Thickening of the muscular walls of the right ventricle due to increased pressure from the obstruction.
  • Ventricular Septal Defect (VSD) - One or more holes in the ventricular septum that allow for abnormal blood flow between the ventricles.
  • Overriding Aorta - A defect where the aorta is positioned above the VSD, receiving blood from both the right and left ventricles.

2. Procedure

The surgical procedure for the complete repair of tetralogy of Fallot without pulmonary atresia involves several critical steps:

  • Accessing the Heart - The heart is exposed through a median sternotomy, allowing the surgeon to access the cardiac structures directly.
  • Establishing Cardiopulmonary Bypass - Cardiopulmonary bypass is initiated to take over the function of the heart and lungs, allowing for a bloodless surgical field while the heart is temporarily stopped using cardioplegic arrest.
  • Repairing the Ventricular Septal Defect (VSD) - The VSD is repaired using a synthetic patch, which closes the defect and prevents the mixing of oxygenated and deoxygenated blood between the ventricles.
  • Addressing Pulmonary Stenosis - The narrowed pulmonary valve is enlarged by resecting obstructive tissue in the right ventricle. If necessary, a transannular patch may be placed to further enlarge the outflow tract.
  • Finalizing the Repair - The surgical team ensures that all defects are corrected, and the heart is restored to normal function before gradually weaning off cardiopulmonary bypass and allowing the heart to resume its natural rhythm.

3. Post-Procedure

After the procedure, the neonate will be closely monitored in a pediatric intensive care unit (PICU) for any complications. Expected recovery includes observation for signs of infection, monitoring of vital signs, and ensuring adequate oxygenation. The surgical team will assess the heart function and may perform echocardiograms to evaluate the success of the repair. Follow-up care will be necessary to monitor the child's growth and development, as well as to manage any long-term effects of the congenital heart defect and the surgical intervention.

Short Descr COMP RPR TOF WO PULM ATRESIA
Medium Descr COMPL RPR TETRALOGY FALLOT W/O PULM ATRESIA
Long Descr Complete repair tetralogy of Fallot without pulmonary atresia;
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 49 - Other OR heart procedures

This is a primary code that can be used with these additional add-on codes.

33257 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure)
33259 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure)
33924 Addon Code MPFS Status: Active Code APC C CPT Assistant Article Ligation and takedown of a systemic-to-pulmonary artery shunt, performed in conjunction with a congenital heart procedure (List separately in addition to code for primary procedure)
34714 Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure)
34716 Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure)
34833 Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure)
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Action
Notes
2025-01-01 Changed Short Description changed.
2010-01-01 Changed Code description changed.
Pre-1990 Added Code added.
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