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Official Description

Repair of complex cardiac anomalies (eg, single ventricle with subaortic obstruction) by surgical enlargement of ventricular septal defect

© Copyright 2025 American Medical Association. All rights reserved.

Common Language Description

A ventricular septal defect (VSD) is defined as an abnormal opening in the interventricular septum, which is the wall separating the left and right ventricles of the heart. This defect allows for the mixing of oxygenated blood from the left ventricle with unoxygenated blood from the right ventricle, leading to inefficient circulation and potential complications. In patients with complex cardiac anomalies, such as a single functioning ventricle, the presence of a smaller underdeveloped ventricle and a small VSD can significantly impair the heart's ability to pump sufficient oxygenated blood to the body. To address this issue, surgical intervention is required to enlarge the VSD, thereby facilitating adequate blood mixing and improving oxygen delivery to systemic circulation. The procedure typically involves a median sternotomy, which provides access to the heart, and the use of cardiopulmonary bypass to maintain circulation during the surgery. The surgical steps include incising the ventricle, enlarging the VSD by cutting into the interventricular septum, and subsequently closing the incision in the ventricle. Following the procedure, cardiopulmonary bypass is discontinued, and chest tubes are placed to manage any fluid accumulation before the chest incision is closed. This surgical repair is critical for patients with complex cardiac conditions to enhance their overall cardiac function and improve their quality of life.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The procedure is indicated for patients with complex cardiac anomalies, particularly those with a single functioning ventricle and associated conditions that necessitate surgical intervention. The following are specific indications for performing the repair of complex cardiac anomalies through the enlargement of a ventricular septal defect:

  • Single Ventricle Condition Patients with a single functioning ventricle, where one ventricle is underdeveloped, require surgical intervention to improve blood flow and oxygenation.
  • Subaortic Obstruction The presence of subaortic obstruction in conjunction with a VSD may necessitate surgical enlargement to facilitate adequate blood mixing and systemic circulation.
  • Severe Symptoms Patients exhibiting severe symptoms related to inadequate oxygenation or heart failure due to the VSD may be candidates for this surgical procedure.

2. Procedure

The surgical procedure for the repair of complex cardiac anomalies through the enlargement of a ventricular septal defect involves several critical steps, each designed to ensure effective correction of the defect and restoration of normal blood flow. The following outlines the procedural steps:

  • Step 1: Median Sternotomy The procedure begins with a median sternotomy, which involves making an incision along the midline of the chest to gain access to the heart. This approach allows the surgeon to visualize and operate on the heart effectively.
  • Step 2: Initiation of Cardiopulmonary Bypass Once access to the heart is achieved, cardiopulmonary bypass is initiated. This technique temporarily takes over the function of the heart and lungs, allowing for a bloodless surgical field and maintaining circulation during the procedure.
  • Step 3: Incision of the Ventricle The surgeon then incises the ventricle to expose the ventricular septal defect. This step is crucial for accessing the area that requires repair.
  • Step 4: Enlargement of the VSD The ventricular septal defect is enlarged by incising the interventricular septum. This enlargement is necessary to facilitate the mixing of oxygenated and unoxygenated blood, which is vital for patients with complex cardiac anomalies.
  • Step 5: Closure of the Ventricle After the VSD has been adequately enlarged, the incision in the ventricle is closed. This step is essential to restore the integrity of the heart structure and ensure proper function.
  • Step 6: Discontinuation of Cardiopulmonary Bypass Following the closure of the ventricle, cardiopulmonary bypass is discontinued, allowing the heart to resume its normal function.
  • Step 7: Placement of Chest Tubes Chest tubes are placed to facilitate the drainage of any fluid that may accumulate in the thoracic cavity post-surgery, which is a standard practice to prevent complications.
  • Step 8: Closure of the Chest Incision Finally, the chest incision is closed, completing the surgical procedure. This step ensures that the surgical site is properly sealed and promotes healing.

3. Post-Procedure

Post-procedure care is critical for ensuring a successful recovery following the surgical enlargement of the ventricular septal defect. Patients are typically monitored closely in a postoperative setting to assess their recovery and manage any potential complications. Expected recovery may include a stay in the intensive care unit (ICU) for monitoring of vital signs, cardiac function, and fluid balance. Pain management is also an essential aspect of post-operative care, as patients may experience discomfort from the surgical incision. The placement of chest tubes will be monitored to ensure proper drainage and prevent fluid accumulation. Patients will be gradually weaned off any mechanical support as their condition stabilizes. Follow-up appointments will be necessary to evaluate the surgical outcome and the overall cardiac function, ensuring that the patient is recovering as expected and that the enlargement of the VSD has effectively improved blood flow and oxygenation.

Short Descr REPAIR BY ENLARGEMENT
Medium Descr RPR CAR ANOMAL SURG ENLGMENT VENTR SEPTL DFCT
Long Descr Repair of complex cardiac anomalies (eg, single ventricle with subaortic obstruction) by surgical enlargement of ventricular septal defect
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 49 - Other OR heart procedures

This is a primary code that can be used with these additional add-on codes.

33257 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure)
33259 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure)
33924 Addon Code MPFS Status: Active Code APC C CPT Assistant Article Ligation and takedown of a systemic-to-pulmonary artery shunt, performed in conjunction with a congenital heart procedure (List separately in addition to code for primary procedure)
34714 Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure)
34716 Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure)
34833 Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure)
Date
Action
Notes
2002-01-01 Changed Code description changed.
1994-01-01 Added First appearance in code book in 1994.
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