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Official Description

Reconstruction of complex cardiac anomaly (eg, single ventricle or hypoplastic left heart) with palliation of single ventricle with aortic outflow obstruction and aortic arch hypoplasia, creation of cavopulmonary anastomosis, and removal of right and left pulmonary bands (eg, hybrid approach stage 2, Norwood, bidirectional Glenn, pulmonary artery debanding)

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Common Language Description

Reconstruction of a complex cardiac anomaly involves a surgical procedure aimed at correcting significant congenital heart defects, particularly those that affect the normal flow of blood through the heart and to the body. This specific procedure, identified by CPT® Code 33622, is typically performed as the second stage of a hybrid approach to treatment. Such anomalies often include conditions like hypoplastic left heart syndrome, where the left side of the heart is underdeveloped, leading to a reliance on the right ventricle to manage both pulmonary and systemic blood flow. The surgical intervention is critical to establish a more balanced circulation, ensuring that adequate blood reaches both the lungs for oxygenation and the rest of the body to support its functions. The procedure is complex and requires careful planning and execution, as it involves multiple steps to reconstruct the heart's anatomy and improve its functionality. The use of median sternotomy allows access to the heart, and techniques such as cardiopulmonary bypass and hypothermic circulatory arrest are employed to facilitate the surgery while minimizing risks to the patient. Overall, this reconstruction aims to enhance the patient's quality of life and improve long-term outcomes for those with severe cardiac anomalies.

© Copyright 2025 Coding Ahead. All rights reserved.

1. Indications

The reconstruction of a complex cardiac anomaly, as described by CPT® Code 33622, is indicated for patients with specific congenital heart defects that require surgical intervention to improve blood flow and heart function. The following conditions are explicitly mentioned as indications for this procedure:

  • Single Ventricle Defect - A condition where one of the heart's ventricles is underdeveloped, leading to inadequate blood circulation.
  • Hypoplastic Left Heart Syndrome - A severe congenital heart defect characterized by the underdevelopment of the left side of the heart, including the left ventricle and aortic arch.
  • Aortic Outflow Obstruction - A blockage that prevents normal blood flow from the heart to the aorta, which can lead to serious complications if not addressed.
  • Aortic Arch Hypoplasia - A condition where the aortic arch is underdeveloped, affecting the distribution of blood to the body.

2. Procedure

The procedure for reconstructing a complex cardiac anomaly involves several critical steps, each designed to address the specific anatomical challenges presented by the patient's condition. The following procedural steps are performed:

  • Step 1: Median Sternotomy - The surgical team begins by making an incision through the sternum to gain access to the heart. This approach allows for optimal visibility and access to the cardiac structures.
  • Step 2: Establishing Cardiopulmonary Bypass - Cardiopulmonary bypass is initiated to take over the function of the heart and lungs during the surgery. This is often accompanied by hypothermic circulatory arrest, which helps to protect the brain and other vital organs during the procedure.
  • Step 3: Atrial Septum Excision - The upper aspect of the heart is incised, and the atrial septum is completely excised to facilitate better blood flow and to prepare for further reconstruction.
  • Step 4: Ductus Arteriosus Management - The previously placed ductus arteriosus stent is removed, and the ductus arteriosus is ligated, divided, and excised to eliminate any abnormal connections that could disrupt normal blood flow.
  • Step 5: Main Pulmonary Artery Division - The main pulmonary artery is divided proximal to the bifurcation, and the distal stump is closed using a pericardial patch or a graft, which may be synthetic or from a cadaver donor.
  • Step 6: Aortic Arch Reconstruction - The undersurface of the aortic arch is opened, extending from the ductus arteriosus along the descending aorta. A cadaver donor pulmonary graft is prepared for anastomosis to enlarge the hypoplastic aortic arch.
  • Step 7: Aortopulmonary Shunt Creation - An aortopulmonary shunt or a conduit from the right ventricle to the pulmonary artery is created to ensure adequate lung perfusion. This is achieved using a synthetic graft placed from either the innominate artery or the right ventricle to the central pulmonary artery.
  • Step 8: Removal of Pulmonary Bands - The previously placed pulmonary artery bands are removed to allow for normal blood flow and pressure regulation.
  • Step 9: Rewarming and Weaning - The patient is gradually rewarmed, and the team weans the patient off cardiopulmonary bypass, ensuring stable hemodynamics before proceeding.
  • Step 10: Closure - Chest tubes are placed to facilitate drainage, and the chest incision is closed securely to complete the procedure.

3. Post-Procedure

After the reconstruction of the complex cardiac anomaly, the patient will require careful monitoring and post-operative care. This includes observation in a critical care setting to assess heart function, manage fluid balance, and monitor for any potential complications. The placement of chest tubes will help drain any excess fluid or blood from the surgical site, promoting healing and reducing the risk of infection. Patients may experience a recovery period that varies in length, depending on their overall health and the complexity of the surgery. Follow-up appointments will be necessary to evaluate the success of the procedure and to monitor the patient's ongoing cardiac function and development.

Short Descr REDO COMPL CARDIAC ANOMALY
Medium Descr RECONSTRUCTION COMPLEX CARDIAC ANOMALY
Long Descr Reconstruction of complex cardiac anomaly (eg, single ventricle or hypoplastic left heart) with palliation of single ventricle with aortic outflow obstruction and aortic arch hypoplasia, creation of cavopulmonary anastomosis, and removal of right and left pulmonary bands (eg, hybrid approach stage 2, Norwood, bidirectional Glenn, pulmonary artery debanding)
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Inpatient Procedures, not paid under OPPS
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 1
CCS Clinical Classification 49 - Other OR heart procedures

This is a primary code that can be used with these additional add-on codes.

33259 Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure)
33768 Addon Code MPFS Status: Active Code APC C Illustration for Code Anastomosis, cavopulmonary, second superior vena cava (List separately in addition to primary procedure)
33924 Addon Code MPFS Status: Active Code APC C CPT Assistant Article Ligation and takedown of a systemic-to-pulmonary artery shunt, performed in conjunction with a congenital heart procedure (List separately in addition to code for primary procedure)
34714 Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure)
34716 Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure)
34833 Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure)
22 Increased procedural services: when the work required to provide a service is substantially greater than typically required, it may be identified by adding modifier 22 to the usual procedure code. documentation must support the substantial additional work and the reason for the additional work (ie, increased intensity, time, technical difficulty of procedure, severity of patient's condition, physical and mental effort required). note: this modifier should not be appended to an e/m service.
51 Multiple procedures: when multiple procedures, other than e/m services, physical medicine and rehabilitation services or provision of supplies (eg, vaccines), are performed at the same session by the same individual, the primary procedure or service may be reported as listed. the additional procedure(s) or service(s) may be identified by appending modifier 51 to the additional procedure or service code(s). note: this modifier should not be appended to designated "add-on" codes (see appendix d).
59 Distinct procedural service: under certain circumstances, it may be necessary to indicate that a procedure or service was distinct or independent from other non-e/m services performed on the same day. modifier 59 is used to identify procedures/services, other than e/m services, that are not normally reported together, but are appropriate under the circumstances. documentation must support a different session, different procedure or surgery, different site or organ system, separate incision/excision, separate lesion, or separate injury (or area of injury in extensive injuries) not ordinarily encountered or performed on the same day by the same individual. however, when another already established modifier is appropriate it should be used rather than modifier 59. only if no more descriptive modifier is available, and the use of modifier 59 best explains the circumstances, should modifier 59 be used. note: modifier 59 should not be appended to an e/m service. to report a separate and distinct e/m service with a non-e/m service performed on the same date, see modifier 25.
80 Assistant surgeon: surgical assistant services may be identified by adding modifier 80 to the usual procedure number(s).
AS Physician assistant, nurse practitioner, or clinical nurse specialist services for assistant at surgery
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2011-01-01 Added Added
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